Cavernous Transformation of Portal Vein

Authors

  • Maria Inês Mascarenhas Departamento de Pediatria. Hospital Prof. Doutor Fernando Fonseca EPE. Amadora. Portugal.
  • Marta Carneiro de Moura Departamento de Pediatria. Hospital Prof. Doutor Fernando Fonseca EPE. Amadora. Portugal.
  • Piedade Sande Lemos Departamento de Pediatria. Hospital Prof. Doutor Fernando Fonseca EPE. Amadora. Portugal.

DOI:

https://doi.org/10.20344/amp.296

Abstract

Introduction: In Cavernous transformation of portal vein (CTPV), therapeutic options are limited; however the restoration of circulation by mesenteric-portal bypass (MPB) is an option in selected cases.

Case Report 1: 13-year-old female with polymalformative syndrome. Admission at 4 months of age to Intensive Care Unit due to severe pneumonia with hemodynamic instability. Follow up due to thrombocytopenia and splenomegalia she was diagnosed CTPV at 7-years old. At 13y-old she was submitted to MPB.

Case Report 2: 9-years-old male; severe neonatal Rh isoimmunization treated with exsanguinations. Followed-up since 6-months of age due to thrombocytopenia and splenomegalia, and at 3 years of age he was diagnosed CTPV. Due to disease progression he was proposed as candidate to MBP which was contraindicated due to vascular thrombosis of the Rex recess.

Comments: MBP presents as one of the few therapeutic options to CTPV in children; due to its specificity and rigid requirements it is vital the close follow up and early diagnosis.

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Published

2012-11-12

How to Cite

1.
Mascarenhas MI, Carneiro de Moura M, Sande Lemos P. Cavernous Transformation of Portal Vein. Acta Med Port [Internet]. 2012 Nov. 12 [cited 2024 Mar. 29];25(5):340-2. Available from: https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/296