MRI Findings in Rasmussen’s Encephalitis

Authors

  • Carolina Mendes Dos Santos Hospital de Santa Maria – Serviço de Imagiologia Neurológica. Centro Hospitalar Lisboa Norte. Lisboa. Portugal.
  • Teresa Moreno Unidade de Neurologia Pediátrica, Serviço de Pediatria. Centro Hospitalar Lisboa Norte. Lisboa. Portugal.
  • Graça Sá Hospital de Santa Maria – Serviço de Imagiologia Neurológica. Centro Hospitalar Lisboa Norte. Lisboa. Portugal.
  • David Rodrigues Hospital de Santa Maria – Serviço de Imagiologia Neurológica. Centro Hospitalar Lisboa Norte. Lisboa. Portugal.
  • Jorge G Campos Hospital de Santa Maria – Serviço de Imagiologia Neurológica. Centro Hospitalar Lisboa Norte. Lisboa. Portugal.

DOI:

https://doi.org/10.20344/amp.276

Abstract

Introduction: Rasmussen’s encephalitis is a chronic inflammatory encephalitis of unknown etiology. Clinical, imaging and electroencephalographic characteristic findings allow its diagnosis. Serial brain MRI evaluation of these patients has a characteristic pattern of temporal evolution. Regarding a clinical case, the authors make a brief review of this pathology, with particular emphasis on the MRI findings.

Case Report: Female child, seven years old, who started a drug-resistent focal epilepsy at the age of four. The video-EEG revealed a left fronto-temporal epileptogenic focus. The serial MRI evaluation showed a left fronto-temporal and insular lesion with variation of its imaging features over time. After thorough investigation, the diagnosis of exclusion was that of Rasmussen’s encephalitis.

Conclusion: MRI plays an important role in the diagnosis and monitoring of Rasmussen’s encephalitis. Regarding a clinical case, we review this pathology, specially its MRI findings.

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Published

2012-11-02

How to Cite

1.
Mendes Dos Santos C, Moreno T, Sá G, Rodrigues D, Campos JG. MRI Findings in Rasmussen’s Encephalitis. Acta Med Port [Internet]. 2012 Nov. 2 [cited 2024 Apr. 19];25:68-72. Available from: https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/276

Issue

Section

Case Report