Hansen’s Disease: An Unusual Manifestation of an Ancient Disease

Authors

DOI:

https://doi.org/10.20344/amp.20599

Keywords:

Arthralgia, Erythema Nodosum, Leprosy, Mycobacterium leprae

Abstract

Hansen’s disease, commonly known as leprosy, is an infectious disease caused by Mycobacterium leprae. Being rare in developed countries, it is an increasingly common imported disease due to the migratory flow from countries where it is endemic. We present the case of a 21-year-old man who went to the emergency department with complaints of additive polyarthralgia involving large joints, papules, and erythematous plaques on the limbs with bullae and central necrosis and fever with chills for one week. Skin biopsy was performed revealing neutrophilic infiltrate with perineural granulomas. The bacilloscopy detected acid-alcohol resistant bacilli. The diagnosis of multibacillary HD with type 2 lepromatous reaction (erythema nodosum leprosum - ENL) was established, showing clinical improvement under corticosteroid therapy. ENL usually presents with painful lesions, being an atypical presentation of leprosy, especially in the presence of bullae and necrosis, making diagnosis difficult and challenging. Social stigma is often present making it difficult to accept the disease as well as adherence to treatment.

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References

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Published

2024-01-25

How to Cite

1.
Ferreira M, Grijó C, Paulo J, Fonseca M, Neves Z, Bouceiro Mendes R, Vasconcelos P. Hansen’s Disease: An Unusual Manifestation of an Ancient Disease. Acta Med Port [Internet]. 2024 Jan. 25 [cited 2024 Jul. 25];37(3):215-9. Available from: https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/20599

Issue

Section

Case Report