Arrhythmogenic Left Ventricular Cardiomyopathy: A Successful Case of Extracorporeal Cardiopulmonary Resuscitation

Authors

  • Mafalda Gama Unidade de Urgência Médica. Centro Hospitalar Universitário de Lisboa Central. Lisbon.
  • Isabel Cardoso Serviço de Cardiologia. Centro Hospitalar Universitário de Lisboa Central. Lisbon.
  • Mónica Palma Anselmo Hospital Professor Doutor Fernando da Fonseca. Lisbon.
  • Sílvia Aguiar Rosa Serviço de Cardiologia. Centro Hospitalar Universitário de Lisboa Central. Lisbon.
  • Pedro Gaspar da Costa Unidade de Urgência Médica. Centro Hospitalar Universitário de Lisboa Central. Lisbon.
  • Philip Fortuna Unidade de Urgência Médica. Centro Hospitalar Universitário de Lisboa Central. Lisbon.

DOI:

https://doi.org/10.20344/amp.19624

Keywords:

Arrhythmogenic Left Ventricular Cardiomyopathy, Cardiopulmonary Resuscitation, Extracorporeal Membrane Oxygenation, Heart Arrest/therapy

Abstract

A 24-year-old man suffered a witnessed cardiac arrest after a padel game. Basic life support was immediately provided. The pre-hospital emergency services team continued the resuscitation efforts, and the patient was accepted for extracorporeal cardiopulmonary resuscitation. The return of spontaneous circulation was achieved in 45 minutes. The initial assessment revealed a ST-segment elevation in leads V4-V6 and a dilated left ventricle with severe systolic dysfunction. Coronary angiography was normal. An improvement in left ventricular systolic function was observed and extracorporeal cardiac support was discontinued after 48 hours. Cardiovascular magnetic resonance imaging demonstrated hypokinesia and subepicardial fatty infiltration of the left ventricle lateral wall. Genetic testing detected a variant of uncertain significance in the ANK2 gene. The diagnosis of arrhythmogenic left ventricular myocardiopathy did not fulfill all the current diagnostic criteria, but it is a very likely diagnosis. An implantable cardioverter-defibrillator was placed. The
patient was discharged without physical or cognitive impairment.

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References

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Published

2023-06-16

How to Cite

1.
Gama M, Cardoso I, Palma Anselmo M, Aguiar Rosa S, Gaspar da Costa P, Fortuna P. Arrhythmogenic Left Ventricular Cardiomyopathy: A Successful Case of Extracorporeal Cardiopulmonary Resuscitation. Acta Med Port [Internet]. 2023 Jun. 16 [cited 2023 Sep. 23];36(9):598-602. Available from: https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/19624

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Section

Case Report