Catastrophic primary antiphospholipid syndrome.

Authors

  • Paula Casanova Serviços de Medicina Intensiva e Anatomia Patológica, Hospitais da Universidade de Coimbra, Coimbra.
  • João P Baptista
  • Maria J Andrade
  • Paulo Martins
  • J P Almeida Sousa
  • Victor Fernandes
  • Armindo Simões
  • Júlio Souto Gonçalves
  • Janeiro Costa
  • Armindo Rebelo
  • Lina Carvalho
  • Jorge Pimentel

DOI:

https://doi.org/10.20344/amp.1179

Abstract

Catastrophic antiphospholipid syndrome develops in a minority of patients with antiphospholipid syndrome, and is characterized by acute thrombotic microvasculopathy with multiorganic involvement (three or more organs). The aetiology is unknown, the diagnosis is complex, and the treatment is empiric, mortality may approach 50%. The authors present a clinical case of catastrophic antiphospholipid syndrome, diagnosed in a patient with abdominal pain and severe respiratory failure.

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How to Cite

1.
Casanova P, Baptista JP, Andrade MJ, Martins P, Almeida Sousa JP, Fernandes V, Simões A, Souto Gonçalves J, Costa J, Rebelo A, Carvalho L, Pimentel J. Catastrophic primary antiphospholipid syndrome. Acta Med Port [Internet]. 2003 Aug. 31 [cited 2024 Apr. 20];16(4):289-94. Available from: https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/1179

Issue

Section

Arquivo Histórico